AR MODARESI; F GHANEH SHERBAF
Volume 12, Issue 4 , January and February 2006, , Pages 53-56
Abstract
Background and purpose: Congenital Lymphedema is a kind of primary Lymphedema caused by on abnormality in the Lymphatic system and causes the Lymph accumulation in the interstitial space. It usually appears within the first two gears of life with mild to severe swelling in one organ together with lethal ...
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Background and purpose: Congenital Lymphedema is a kind of primary Lymphedema caused by on abnormality in the Lymphatic system and causes the Lymph accumulation in the interstitial space. It usually appears within the first two gears of life with mild to severe swelling in one organ together with lethal complications and disseminated as it may be misdiagnosed with acquired edematous diseases particularly in infancy, this, case report is intended to present the disease with clinical indices and paraclinical evaluation.
Case report: A fourteen–month-old patient suffering from congenital Lymphedema is reported here who had been referred to Dr.sheik Hospital in Mashad, Iran as nephritic syndrome. The case was treated after congenital Lymphedema diagnosis was established.
Conclusion: Congenital Lymphedema is often mistaken with acquired edematous diseases and particularly in infancy with nephritic syndrome. There fore, the knowledge of clinical indices and paraclinical evaluation are necessary for perfect diagnosis.